Celiac disease as a potential cause of idiopathic portal hypertension: a case report
Farhad Zamani, Afsaneh Amiri, Ramin Shakeri, Ali Zare, Mehdi Mohamadnejad
Gastrointestinal and Liver Disease Research Center, and 3Dept. Pathology, Firouzgar Hospital, Iran University of Medical Sciences, Tehran, Iran, Digestive Disease Research Center, Shariati Hospital, Tehran University of Medical Sciences, Tehran, Iran
A 54-year-old man was admitted to our hospital for evaluation of malaise, weight loss, abdominal swelling and lower limb edema. His para-clinical tests revealed pancytopenia, large ascites, splenomegaly and esophageal varices consistent with portal hypertension. Duodenal biopsy and serologic findings were compatible with celiac disease. His symptoms improved on a gluten-free diet, but his clinical course was further complicated with ulcerative jejuno-ileitis, and intestinal T-cell lymphoma.
This article was published in Journal of Medical Case Reports 2009, 3:68. This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/2.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
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